Hydroxysteroid (17 beta) Dehydrogenase 4 (HSD17B4) Mouse Monoclonal Antibody [Clone ID: LBI4C4]
产品名称: Hydroxysteroid (17 beta) Dehydrogenase 4 (HSD17B4) Mouse Monoclonal Antibody [Clone ID: LBI4C4]
英文名称: Hydroxysteroid (17 beta) Dehydrogenase 4 (HSD17B4) Mouse Monoclonal Antibody [Clone ID: LBI4C4]
产品编号: AMM14107V
产品价格: null
产品产地: 美国
品牌商标: Leading Biology
更新时间: null
使用范围: WB 1:4000, IF 1:100, IHC 1:150
安诺伦(北京)生物科技有限公司
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别名:DBP; MFE-2; MPF-2; PRLTS1; SDR8C1 产品概述:HSD17B4 mouse monoclonal antibody, clone LBI4C4 总结:The protein encoded by this gene is a bifunctional enzyme that is involved in the peroxisomal beta-oxidation pathway for fatty acids. It also acts as a catalyst for the formation of 3-ketoacyl-CoA intermediates from both straight-chain and 2-methyl-branched-chain fatty acids. Defects in this gene that affect the peroxisomal fatty acid beta-oxidation activity are a cause of D-bifunctional protein deficiency (DBPD). An apparent pseudogene of this gene is present on chromosome 8. [provided by RefSeq, Jul 2008]